BopheloMafu a le Maemo

Wegener o granulomatosis - Sesosa, matšoao, kalafo.

granulomatosis Wegener o - e le lefu autoimmune tšoauoa ka ho ruruha ea methapo tse nyenyane le methapong. Maemong a mangata ho mothapo ruruhileng fa mali sinuses, matšoafo le liphio lisele empa, ho phaella moo, ho na le dibopeho tsena leeme ka ketsahalo eo e amang e 'ngoe ea ka libaka tsena feela. Ka granulomatosis a pharaletseng a hoo e ka bang kamehla ba tsota matšoafo bobeli le liphio tse peli. Boemong bo joalo, haeba ho ameha ke khanya feela kapa feela liphio, e ke lefu le bitsoang granulomatosis Wegener o fella.

granulomatosis Wegener ke atileng ka ho fetisisa ho batho ba ka tlaase kapa bohareng-ba hōlileng, hoo e ka bang ntle le ho kopana le bana. Empa, leha ho le joalo, lefu ke kgona ho ama lihlopha tsohle lilemo. Lipalo-palo bong hlōla lefu lena fapane ka bangodi fapaneng.

Lisosa tsa lefu lena

Lisosa tsa mafu a joalo, tse kang granulomatosis Wegener o, kajeno e sa utloisise ka ho feletseng. Litsebi tse ngata li lumela hore sesosa sa lefu lena ka 'na ba le moemeli bongata ba kokwanahloko, hobane granulomatosis Wegener hangata le hlaha ka mor'a ente, SARS, lithibela-mafu phekolo kapa kgahlamelo ya maqhubu a. Empa, ka bomalimabe, e moemeli likokoana-hloko tse se ntse se abelwa, kahoo lefu lena le nkoa e le autoimmune.

Ba bang bakuli ba ferekanya poradenitis le granulomatosis Wegener o. E lokela ho utloisisa hore ho tšoana ho ba le matšoao a ho nang le ba babeli le mafu a fapaneng ka ho feletseng ka lebaka poradenitis hlaha ka lebaka la ho likokoana-hloko baktheria (Chlamydia), ha a ntse a granulomatosis Wegener ke lefu le autoimmune.

Le matšoao 'me mofuta o lefu

granulomatosis Wegener o ka qala ka tšohanyetso, empa ka 'na diablo ho fihlela butle-butle. Le letšoao la pele lefu lena ka nkoa subfebrile mocheso, ka nako eo ho fokotsa takatso ea lijo. Ka mor'a moo mocheso le qala ho tsoha, le tsoelo-pele ea lefu.

Matšoao a tloaelehileng a lefu lena kenyeletsa:

- boima ba 'mele ke tahlehelo;

- mokhathala;

- hōlisa mocheso;

- bohloko manonyeletso;

- bohloko ka ho ruruha sinus.

Ho phaella moo, lefu lena le ka ama likarolo tse sa tšoaneng tsa 'mele, a fana ka matšoao a fapaneng ka ho feletseng. Ka mohlala, ka ho hlōloa ha Link matšoafo runny nko le bothatanyana purulent likarohano tšollang mali, necrotic nasal mucosa, hammoho le mahalapa a le bonolo 'me tonsils.

A foromo generalized ya lefu lena le fana ka likhoeli tse seng kae, e complication e tebileng ea letlalo, ka ho khetheha, bonahala tsoa mali, nodular, likarolo necrotic, 'me ka ba bang ba lihlopha tsa bakuli,' me pericarditis, myocarditis kapa la bronchitis.

phumano ya lefu lena

Haholo-holo bakeng sa belaela Wegener o granulomatosis bakuli lokela feta urinalysis bakeng sa ho ba teng ha lisele tsa protheine le mali tse khubelu ka moroto wa. Ho ekelletsa moo X-ray Litšoantšo tse entsoeng sinuses le sefubeng, ho bona liphetoho pathological. Ho feta moo, ho hlahloba mali a nkiloeng 'me, ka ho khetheha, e laolwang ke ESR le C-arabelang protheine. Ho na le boetse ho na le ho feta, empa hape atlehang haholoanyane and analysis ho khetholla antineyrofilnyh lisireletsi cytoplasmic.

kalafo ea lefu lena

granulomatosis Wegener o, ntle le kalafo e nepahetseng ho ba le mamello ka 'na lebisa ho lefu ka hare ho likhoeli tse peli ho isa ho tse tharo. kalafo bohle e haholo-holo ikemiseditse ho ea hatelloang ya boitshireletso ba mmele, hammoho le ea moo liphetoho a hlabang. The lithethefatsi ho fetisisa ratoa ke corticosteroids le cyclophosphamide. lithethefatsi tsena li ka ba lokela ho ho nkoa ka ho fihlela ho leballa motho ea lefu lena, 'me ntan'o ba ho ke ke ua khutlela mokhoeng oo lefu Hodgkin, e ka ho phaella ka ho re ho bona leha ho le joalo le methotrexate, e leng lokela ho nka e le banyalani ba bang ba tsa lilemo.

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