Lennox-Gastaut lefu (sethoathoa)

Lennox-Gastaut lefu - mofuta o mong oa lefu la sethoathoa (myoclonic-astatic). Joalo mafu mothofatso akarelletsa ha e kopana le tonic le sethoathoa atonic, atypical sieo sethoathoa, lieha ntshetsopele ya bokgoni ba kelello ho masea. Ka lekhetlo la pele lefu lena le ka iponahatsa ka bana ba tsoang ho e 'ngoe ho tse hlano, haholo-holo bakeng sa bashanyana.

lefu lena hangata develops ka lebaka isoa bongoaneng mafu methapo ea kutlo, 'me ho qala ka lerotholi ka tšohanyetso ka ngoana. Ka mor'a nako e itseng, ho na le tsitsipana, sethoathoa, bontša lieha ntshetsopeleng kelellong le fokotswa bohlale.

Butle-butle, le kgolo ya ngoana, mofuta wa sethoathoa fapana. Fall nkeloa sebaka ke a leeme, ba bobedi generalized, litlhaselo rarahaneng ea lefu la sethoathoa.

Ka lebaka la seo se bontšoa lefu Lennox-Gastaut

Ho utloisisa lintho tse bakelang lefu lena ke ho le thata ka ho lekaneng, empa ho letsatsi tsebahalang ke bona ba ka sehloohong.

• The anomaly ya ntshetsopele boko.
• tsoaetsanang haholo (meningitis, ho ruruha ha boko, rubella).
• Liphatseng tsa lefutso mafu pathological boko (CNS, mafu tshilong ya dijo, tuberculous sclerosis).
• ngoana lemetseng nakong temana ea kanale tsoalo (tsoalo asphyxia, tsoalo pele ho nako, joalo-joalo).
• CNS mo ntša kotsi ka nako perinatal, hammoho le preterm pelehi le asphyxia.

matšoao a PLGA

Lennox-Gastaut syndrome, ka o ile a hlokomela ke letšoao bohlokoa ka ho fetisisa - bakeng sa sethoathoa. Bana ba na le boloetse ba "idiopathic sethoathoa", hape e bua ka mefuta e sa tšoaneng ea lefu la sethoathoa (matšoao a) :

• paroxysms tsa liphororong;
• atonic sethoathoa;
• atypical absences;
• leeme sethoathoa;
• sternocleidomastoid cramps;
• myoclonic-astatic sethoathoa;
• tonic sethoathoa (hangata etsahala nakong boroko bo tebileng);
• TC generalized sethoathoa.

Bakuli ba le lefu la Lennox-Gastaut hape ba le boemo bath ya stupor le phetoho boreleli ka lefu la sethoathoa, kholofalo kelellong, dikopanothutano le mafu a botho.

Diagnosing ea syndrome, LH

Hang ka mor'a hore matšoao a pele a lefu o lokela ho hang-hang ho batla thuso ea litsebi, letsetsa ambulense. Ka tloaelo ho, phumano ya lefu lena le o etsoang ho tsoa ho sebedisa ECG pakeng tsa litlhaselo tsa.

LH Syndrome Phekolo

lefu Lennox-Gastaut e tšoaroa ka meriana le mekhoa ea ho buoa. Kalafo le meriana ho hlahisa litholoana tse ntle ha ho ho feta 20% ea linyeoe. Ka ho buoa mokhoa kalafo bakeng sa ho felisa marotholi tšohanyetso, e atlehang ea ho khaola ea polokelo callosum (callosotomy). Hape, tšebeliso tshebetso ile a laela ho tlhotlheletso ya methapo ea kutlo vagus le tlosa lihlahala vascular le malformations.

Leha ho le joalo, re lokela ho hlokomela hore sethoathoa bath ya lefu lena hangata ho bang thata ho tšoara; qetellong ba ka 'na etsa hore mokuli hore litholoana tse bosula sechabeng le kelellong. Hoo e batlang e untreatable tonic sethoathoa, eo lebisa bohlale theola.